Table 1 Overview table for ISSVA classification of vascular anomalies

Benign

Simple

Combined

Of major named vessels

Associated with other anomalies

Capillary malformations (CM)

Associate two or more vascular malformations in one lesion

Affect veins, arteries, or lymphatics of generally large caliber, often axial or conducting vessels

Syndromes in which vascular malformations are accompanied by other symptoms in addition to vascular anomalies

Locally aggressive or borderline

Lymphatic malformations (LM)

Venous malformations (VM)

Malignant

Arteriovenous malformations (AVM)

Arteriovenous fistula (AVF)